ABSTRACT
The desmoid tumors are rare benign fibrous tumors, its intra-thoracic localization is exceptional. Authors report three cases of intra-thoracic tumors, 2 of them were operated. The cases were 3 females, aged 27 to 32 years old, with a mean age of 29,6 years. The symptomatology was silent, in all of them, dominated by chest pain, one case had a palpable mass. The radiological examination did not show a suggestive evocative aspect. The diagnosis depends on the histological findings 2 cases have been operated, and despite the carcinologic resection, relapse occurred in one patient after 9 months. Due to the tumor extensive and infiltrative character its illdefined limits, the third case had only a radiochemotherapy treatment. Our series shows the importance of a well knowledge of these rare tumors, before any therapeutic surgical treatment decision
ABSTRACT
The fibrous osseous dysplasia is a rare congenital condition characterised by the replacement of the medullary canal spongy os by a fibrous tissue proliferation. we reported a case of a young girl, 21 years old, who suffered from thoracic pain since more than one year, with apparation of the axillary arch which progressivaly increase in volume since six months. Examination revealed a fixed hard tumefaction, the thoracic radiography showed two souffle osteolytic images near the medium arc of the fifth left rib and fourth right rib. The osseous scintigraphy revealed an hyperfixation touching the right hemiface. The cranio-facial scan showed an interesting aspect of [frosted glass] of the clivus. The remodeling mark dosage of the osseous alkaline phosphatase was of 2321U/L. A mass biopsy was done which confirmed the diagnosis. the combination of costal and clivus fibrous dysplasia which had been never reported in literatures and the difficult therapeutic decision in front of this polystotic picture makes our case a particular case